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Erdheim–Chester Disease With Multiorgan Involvement, Following Polycythemia Vera: A Case Report

Erdheim–Chester disease is a rare form of non-Langerhans cell histiocytosis characterized by the migration and infiltration of lipid-laden CD68(+), CD1a(−) and S100(−) histiocytes to various target organs, which leads to the disruption of physiological tissue architecture and reactive fibrosis, and...

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Detalhes bibliográficos
Publicado no:Medicine (Baltimore)
Main Authors: Iurlo, Alessandra, Dagna, Lorenzo, Cattaneo, Daniele, Orofino, Nicola, Bianchi, Paola, Cavalli, Giulio, Doglioni, Claudio, Gianelli, Umberto, Cortelezzi, Agostino
Formato: Artigo
Idioma:Inglês
Publicado em: Wolters Kluwer Health 2016
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4902423/
https://ncbi.nlm.nih.gov/pubmed/27196481
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/MD.0000000000003697
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