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All-Atom Simulations Reveal How Single-Point Mutations Promote Serpin Misfolding

Protein misfolding is implicated in many diseases, including serpinopathies. For the canonical inhibitory serpin α(1)-antitrypsin, mutations can result in protein deficiencies leading to lung disease, and misfolded mutants can accumulate in hepatocytes, leading to liver disease. Using all-atom simul...

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Bibliografski detalji
Izdano u:Biophys J
Glavni autori: Wang, Fang, Orioli, Simone, Ianeselli, Alan, Spagnolli, Giovanni, a Beccara, Silvio, Gershenson, Anne, Faccioli, Pietro, Wintrode, Patrick L.
Format: Artigo
Jezik:Inglês
Izdano: The Biophysical Society 2018
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC5961751/
https://ncbi.nlm.nih.gov/pubmed/29742402
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.bpj.2018.03.027
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