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Favorable effect of bortezomib in dense deposit disease associated with monoclonal gammopathy: a case report

BACKGROUND: Complement component 3 (C3) glomerulopathy, which includes dense deposit disease (DDD) and C3 glomerulonephritis, is caused by dysregulation of the alternative complement pathway. In most cases, C3 glomerulopathy manifests pathologically with membranoproliferative glomerulonephritis-like...

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Dades bibliogràfiques
Publicat a:BMC Nephrol
Autors principals: Hirashio, Shuma, Satoh, Ayaka, Arima, Takahiro, Mandai, Kouichi, Awaya, Tadasuke, Oshima, Kumi, Hara, Shigeo, Masaki, Takao
Format: Artigo
Idioma:Inglês
Publicat: BioMed Central 2018
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5934801/
https://ncbi.nlm.nih.gov/pubmed/29724182
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12882-018-0905-6
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