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Autoimmune pulmonary alveolar proteinosis in an adolescent successfully treated with inhaled rhGM-CSF (molgramostim)

Autoimmune pulmonary alveolar proteinosis (aPAP) is a rare parenchymal lung disease characterized by accumulation of surfactant in the airways with high levels of granulocyte-macrophage colony stimulating factor (GM-CSF) antibodies in blood. Disease leads to hypoxemic respiratory failure. Whole lung...

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Detalles Bibliográficos
Publicado en:Respir Med Case Rep
Main Authors: Gajewska, Marta E., Sritharan, Sajitha S., Santoni-Rugiu, Eric, Bendstrup, Elisabeth M.
Formato: Artigo
Idioma:Inglês
Publicado: Elsevier 2018
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC5925949/
https://ncbi.nlm.nih.gov/pubmed/29719809
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.rmcr.2018.02.005
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