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Carotid strain measurement in patients with pseudoxanthoma elasticum — Hint for a different pathomechanism?

Pseudoxanthoma Elasticum (PXE), caused by autosomal-recessive mutations in the ATP-binding cassette transporter (ABCC6) gene, is known for high prevalence of atherosclerosis. A novel method investigating elastic properties of arteries in atherosclerotic patients is vascular strain analysis. We compa...

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Bibliografski detalji
Izdano u:Intractable Rare Dis Res
Glavni autori: Passon, Sebastian Gorgonius, Küllmar, Viviane, Blatzheim, Anna Katharina, Pausewang, Kristin Solveig, Stumpf, Max Jonathan, Hendig, Doris, Gliem, Martin, Pingel, Simon, Schueler, Robert, Skowasch, Dirk, Schahab, Najib, Nickenig, Georg, Schaefer, Christian Alexander
Format: Artigo
Jezik:Inglês
Izdano: International Research and Cooperation Association for Bio & Socio-Sciences Advancement 2018
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC5849621/
https://ncbi.nlm.nih.gov/pubmed/29552442
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.5582/irdr.2018.01004
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