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Carotid strain measurement in patients with pseudoxanthoma elasticum — Hint for a different pathomechanism?

Pseudoxanthoma Elasticum (PXE), caused by autosomal-recessive mutations in the ATP-binding cassette transporter (ABCC6) gene, is known for high prevalence of atherosclerosis. A novel method investigating elastic properties of arteries in atherosclerotic patients is vascular strain analysis. We compa...

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Detalles Bibliográficos
Publicado en:Intractable Rare Dis Res
Main Authors: Passon, Sebastian Gorgonius, Küllmar, Viviane, Blatzheim, Anna Katharina, Pausewang, Kristin Solveig, Stumpf, Max Jonathan, Hendig, Doris, Gliem, Martin, Pingel, Simon, Schueler, Robert, Skowasch, Dirk, Schahab, Najib, Nickenig, Georg, Schaefer, Christian Alexander
Formato: Artigo
Idioma:Inglês
Publicado: International Research and Cooperation Association for Bio & Socio-Sciences Advancement 2018
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC5849621/
https://ncbi.nlm.nih.gov/pubmed/29552442
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.5582/irdr.2018.01004
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