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Replacing a phosphodiesterase-5 inhibitor with riociguat in patients with connective tissue disease-associated pulmonary arterial hypertension: a case series

Patients with pulmonary arterial hypertension associated with connective tissue disease (PAH-PAH-CTD) such as systemic sclerosis (SSc) have a poorer response to treatment and increased mortality compared with patients with idiopathic PAH. Current treatment options for PAH-CTD include prostanoids, ph...

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Detalhes bibliográficos
Publicado no:Pulm Circ
Main Authors: Raina, Amresh, Benza, Raymond L., Farber, Harrison W.
Formato: Artigo
Idioma:Inglês
Publicado em: SAGE Publications 2017
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5841890/
https://ncbi.nlm.nih.gov/pubmed/28671485
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1177/2045893217721694
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