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Hemophagocytic lymphohistiocytosis in an adult kidney transplant recipient successfully treated by plasmapheresis: A case report and review of the literature

RATIONALE: Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening disease entity primarily described in children, but not less relevant in adults. It is characterized by a misdirected activation of the immune system, resulting in an uncontrolled cytokine release from macrophages and cytotoxi...

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Publicado en:Medicine (Baltimore)
Autores principales: Nusshag, Christian, Morath, Christian, Zeier, Martin, Weigand, Markus A., Merle, Uta, Brenner, Thorsten
Formato: Artigo
Lenguaje:Inglês
Publicado: Wolters Kluwer Health 2017
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC5815798/
https://ncbi.nlm.nih.gov/pubmed/29390386
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/MD.0000000000009283
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