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Hemophagocytic lymphohistiocytosis in an adult kidney transplant recipient successfully treated by plasmapheresis: A case report and review of the literature

RATIONALE: Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening disease entity primarily described in children, but not less relevant in adults. It is characterized by a misdirected activation of the immune system, resulting in an uncontrolled cytokine release from macrophages and cytotoxi...

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Publicat a:Medicine (Baltimore)
Autors principals: Nusshag, Christian, Morath, Christian, Zeier, Martin, Weigand, Markus A., Merle, Uta, Brenner, Thorsten
Format: Artigo
Idioma:Inglês
Publicat: Wolters Kluwer Health 2017
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5815798/
https://ncbi.nlm.nih.gov/pubmed/29390386
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/MD.0000000000009283
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