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Identification of Novel Mitochondrial Localization Signals in Human Tafazzin, the Cause of the Inherited Cardiomyopathic Disorder Barth Syndrome

Mutations in the gene tafazzin (TAZ) result in Barth syndrome (BTHS). Patients present with hypotonia, cyclic neutropenia, 3-methyglutaconic aciduria, and cardiomyopathy, which is the major cause of mortality. The recessive, X-linked TAZ gene encodes a mitochondrial membrane-associated phospholipid...

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Detalhes bibliográficos
Publicado no:J Mol Cell Cardiol
Main Authors: Dinca, Ana A., Chien, Wei-Ming, Chin, Michael T.
Formato: Artigo
Idioma:Inglês
Publicado em: 2017
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5801207/
https://ncbi.nlm.nih.gov/pubmed/29129703
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.yjmcc.2017.11.005
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