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Nuclear genes involved in mitochondrial diseases caused by instability of mitochondrial DNA

Mitochondrial diseases are defined by a respiratory chain dysfunction and in most of the cases manifest as multisystem disorders with predominant expression in muscles and nerves and may be caused by mutations in mitochondrial (mtDNA) or nuclear (nDNA) genomes. Most of the proteins involved in respi...

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Publicat a:J Appl Genet
Autors principals: Rusecka, Joanna, Kaliszewska, Magdalena, Bartnik, Ewa, Tońska, Katarzyna
Format: Artigo
Idioma:Inglês
Publicat: Springer Berlin Heidelberg 2018
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5799321/
https://ncbi.nlm.nih.gov/pubmed/29344903
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s13353-017-0424-3
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