Carregant...

Germline TTN variants are enriched in PTEN-wildtype Bannayan–Riley–Ruvalcaba syndrome

Bannayan–Riley–Ruvalcaba syndrome (BRRS) is a rare congenital disorder classically characterized by macrocephaly in combination with intestinal hamartomatous polyposis, vascular malformations, lipomas, and genital lentiginosis. Germline PTEN mutations have been reported in up to 60% of BRRS patients...

Descripció completa

Guardat en:
Dades bibliogràfiques
Publicat a:NPJ Genom Med
Autors principals: Yehia, Lamis, Ni, Ying, Eng, Charis
Format: Artigo
Idioma:Inglês
Publicat: Nature Publishing Group UK 2017
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5735137/
https://ncbi.nlm.nih.gov/pubmed/29263846
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41525-017-0039-y
Etiquetes: Afegir etiqueta
Sense etiquetes, Sigues el primer a etiquetar aquest registre!