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Proteinopathies and OXPHOS dysfunction in neurodegenerative diseases

Mitochondria participate in essential processes in the nervous system such as energy and intermediate metabolism, calcium homeostasis, and apoptosis. Major neurodegenerative diseases are characterized pathologically by accumulation of misfolded proteins as a result of gene mutations or abnormal prot...

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Détails bibliographiques
Publié dans:J Cell Biol
Auteurs principaux: Kawamata, Hibiki, Manfredi, Giovanni
Format: Artigo
Langue:Inglês
Publié: The Rockefeller University Press 2017
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC5716291/
https://ncbi.nlm.nih.gov/pubmed/29167179
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1083/jcb.201709172
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