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Proteinopathies and OXPHOS dysfunction in neurodegenerative diseases

Mitochondria participate in essential processes in the nervous system such as energy and intermediate metabolism, calcium homeostasis, and apoptosis. Major neurodegenerative diseases are characterized pathologically by accumulation of misfolded proteins as a result of gene mutations or abnormal prot...

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Detalhes bibliográficos
Publicado no:J Cell Biol
Main Authors: Kawamata, Hibiki, Manfredi, Giovanni
Formato: Artigo
Idioma:Inglês
Publicado em: The Rockefeller University Press 2017
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5716291/
https://ncbi.nlm.nih.gov/pubmed/29167179
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1083/jcb.201709172
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