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RARE-04. SYNCHRONOUS CENTRAL NERVOUS SYSTEM (CNS) ATYPICAL TERATOID/ RHABDOID TUMOR (AT/RT) AND A MALIGNANT RHABDOID TUMOR OF THE KIDNEY- CASE REPORT OF A LONG-TERM SURVIVOR AND A REVIEW OF THE LITERATURE
BACKGROUND: Central nervous system (CNS) atypical teratoid/rhabdoid tumor (AT/RT) with synchronous or metachronous extra-CNS tumors are extremely rare in children. The majority have a germline mutation in the SMARCB1 gene and a very poor outcome. METHODS: We report one of longest surviving cases in...
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| Vydáno v: | Neuro Oncol |
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| Hlavní autoři: | , , , , , , , , , , , , |
| Médium: | Artigo |
| Jazyk: | Inglês |
| Vydáno: |
Oxford University Press
2017
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| Témata: | |
| On-line přístup: | https://ncbi.nlm.nih.gov/pmc/articles/PMC5692699/ https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/neuonc/nox168.857 |
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