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In vitro modeling of experimental succinic semialdehyde dehydrogenase deficiency (SSADHD) using brain-derived neural stem cells
We explored the utility of neural stem cells (NSCs) as an in vitro model for evaluating preclinical therapeutics in succinic semialdehyde dehydrogenase-deficient (SSADHD) mice. NSCs were obtained from aldh5a1(+/+) and aldh5a1(-/-) mice (aldh5a1 = aldehyde dehydrogenase 5a1 = SSADH). Multiple paramet...
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| Опубликовано в: : | PLoS One |
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| Главные авторы: | , , , , , |
| Формат: | Artigo |
| Язык: | Inglês |
| Опубликовано: |
Public Library of Science
2017
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| Предметы: | |
| Online-ссылка: | https://ncbi.nlm.nih.gov/pmc/articles/PMC5650182/ https://ncbi.nlm.nih.gov/pubmed/29053743 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0186919 |
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