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Hutchinson-Gilford Progeria Is a Skeletal Dysplasia

Hutchinson-Gilford Progeria Syndrome (HGPS) is a rare segmental premature aging disorder that affects bone and body composition, among other tissues. We sought to determine if bone density and structural geometry are altered in children with HGPS, and whether relationships exist among these paramete...

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Publicat a:J Bone Miner Res
Autors principals: Gordon, Catherine M., Gordon, Leslie B., Snyder, Brian D., Nazarian, Ara, Quinn, Nicolle, Huh, Susanna, Giobbie-Hurder, Anita, Neuberg, Donna, Cleveland, Robert, Kleinman, Monica, Miller, David T., Kieran, Mark W.
Format: Artigo
Idioma:Inglês
Publicat: 2011
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5650062/
https://ncbi.nlm.nih.gov/pubmed/21445982
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/jbmr.392
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