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Inhibiting persistent inward sodium currents prevents myotonia

OBJECTIVE: Patients with myotonia congenita have muscle hyperexcitability due to loss‐of‐function mutations in the ClC‐1 chloride channel in skeletal muscle, which causes involuntary firing of muscle action potentials (myotonia), producing muscle stiffness. The excitatory events that trigger myotoni...

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Détails bibliographiques
Publié dans:Ann Neurol
Auteurs principaux: Hawash, Ahmed A., Voss, Andrew A., Rich, Mark M.
Format: Artigo
Langue:Inglês
Publié: John Wiley and Sons Inc. 2017
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC5639374/
https://ncbi.nlm.nih.gov/pubmed/28833464
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/ana.25017
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