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COLLAGEN V HAPLOINSUFFICIENCY IN A MURINE MODEL OF CLASSIC EHLERS-DANLOS SYNDROME IS ASSOCIATED WITH DEFICIENT STRUCTURAL AND MECHANICAL HEALING IN TENDONS

Classic Ehlers-Danlos syndrome (EDS) patients suffer from connective tissue hyperelasticity, joint instability, skin hyperextensibility, tissue fragility, and poor wound healing due to heterozygous mutations in COL5a1 or COL5a2 genes. This study investigated the roles of collagen V in establishing s...

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Detaylı Bibliyografya
Yayımlandı:J Orthop Res
Asıl Yazarlar: Johnston, Jessica M., Connizzo, Brianne K., Shetye, Snehal S., Robinson, Kelsey A., Huegel, Julianne, Rodriguez, Ashley B., Sun, Mei, Adams, Sheila M., Birk, David E., Soslowsky, Louis J.
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: 2017
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC5632109/
https://ncbi.nlm.nih.gov/pubmed/28387435
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/jor.23571
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