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Development of a Tandem Mass Spectrometry Method for Rapid Measurement of Medium- and Very-Long-Chain Acyl-CoA Dehydrogenase Activity in Fibroblasts

Mitochondrial fatty acid oxidation is a vital biochemical process for energy metabolism. Among the known fatty-acid metabolism disorders, very-long-chain acyl-CoA dehydrogenase (VLCAD) deficiency and medium-chain acyl-CoA dehydrogenase (MCAD) deficiency count among the most frequent. Both are potent...

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Publicat a:JIMD Rep
Autors principals: Bouvier, Damien, Vianey-Saban, Christine, Ruet, Séverine, Acquaviva, Cécile
Format: Artigo
Idioma:Inglês
Publicat: Springer Berlin Heidelberg 2016
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5585096/
https://ncbi.nlm.nih.gov/pubmed/27943070
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/8904_2016_22
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