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A severe genotype with favourable outcome in very long chain acyl-CoA dehydrogenase deficiency

A patient with very long chain acyl-CoA dehydrogenase (VLCAD) deficiency is reported. He had a severe neonatal presentation and cardiomyopathy. He was found to be homozygous for a severe mutation with no residual enzyme activity. Tandem mass spectrometry on dried blood spots revealed increased long...

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Main Authors: Touma, E, Rashed, M, Vianey-Saban, C, Sakr, A, Divry, P, Gregersen, N, Andresen, B
פורמט: Artigo
שפה:Inglês
יצא לאור: BMJ Group 2001
נושאים:
גישה מקוונת:https://ncbi.nlm.nih.gov/pmc/articles/PMC1718627/
https://ncbi.nlm.nih.gov/pubmed/11124787
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/adc.84.1.58
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