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Decreased activity of plasma ADAMTS13 are related to enhanced cytokinemia and endotoxemia in patients with acute liver failure

Deficient ADAM metalloproteinase with thrombospondin type-1 motif, member 13 (ADAMTS13) activity (ADAMTS13:AC) results in the accumulation of unusually large von Willebrand factor multimers (UL-VWFM) and causes microcirculatory disturbances and multiple organ failure, while endotoxins trigger the ac...

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Dettagli Bibliografici
Pubblicato in:Biomed Rep
Autori principali: Takaya, Hiroaki, Yoshiji, Hitoshi, Kawaratani, Hideto, Sakai, Kazuya, Matsumoto, Masanori, Fujimura, Yoshihiro, Fukui, Hiroshi
Natura: Artigo
Lingua:Inglês
Pubblicazione: D.A. Spandidos 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5582607/
https://ncbi.nlm.nih.gov/pubmed/28894574
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3892/br.2017.945
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