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Severe Hepatopulmonary Syndrome in a Child with Caroli Syndrome

Hepatopulmonary Syndrome (HPS) is a potential complication of chronic liver disease and is more commonly seen in the adult population. Caroli Syndrome is a rare inherited disorder characterized by intrahepatic ductal dilation and liver fibrosis that leads to portal hypertension. In children with liv...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:Case Rep Pediatr
Egile Nagusiak: De Jesus-Rojas, W., McBeth, K., Yadav, A., Stark, J. M., Mosquera, R. A., Jon, C.
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: Hindawi 2017
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC5572614/
https://ncbi.nlm.nih.gov/pubmed/28884036
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2017/2171974
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