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Severe Hepatopulmonary Syndrome in a Child with Caroli Syndrome
Hepatopulmonary Syndrome (HPS) is a potential complication of chronic liver disease and is more commonly seen in the adult population. Caroli Syndrome is a rare inherited disorder characterized by intrahepatic ductal dilation and liver fibrosis that leads to portal hypertension. In children with liv...
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| Vydáno v: | Case Rep Pediatr |
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| Hlavní autoři: | , , , , , |
| Médium: | Artigo |
| Jazyk: | Inglês |
| Vydáno: |
Hindawi
2017
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| Témata: | |
| On-line přístup: | https://ncbi.nlm.nih.gov/pmc/articles/PMC5572614/ https://ncbi.nlm.nih.gov/pubmed/28884036 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2017/2171974 |
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