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An update on the use of benzoate, phenylacetate and phenylbutyrate ammonia scavengers for interrogating and modifying liver nitrogen metabolism and its implications in urea cycle disorders and liver disease

INTRODUCTION: Ammonia-scavenging drugs, benzoate and phenylacetate (PA)/phenylbutyrate (PB), modulate hepatic nitrogen metabolism mainly by providing alternative pathways for nitrogen disposal. AREAS COVERED: We review the major findings and potential novel applications of ammonia-scavenging drugs,...

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Dettagli Bibliografici
Pubblicato in:Expert Opin Drug Metab Toxicol
Autori principali: de las Heras, Javier, Aldámiz-Echevarría, Luis, Martínez-Chantar, María-Luz, Delgado, Teresa C.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2016
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5568887/
https://ncbi.nlm.nih.gov/pubmed/27860485
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1080/17425255.2017.1262843
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