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A Patient with MSUD: Acute Management with Sodium Phenylacetate/Sodium Benzoate and Sodium Phenylbutyrate

In treatment of metabolic imbalances caused by maple syrup urine disease (MSUD), peritoneal dialysis, and hemofiltration, pharmacological treatments for elimination of toxic metabolites can be used in addition to basic dietary modifications. Therapy with sodium phenylacetate/benzoate or sodium pheny...

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Detalhes bibliográficos
Publicado no:Case Rep Pediatr
Main Authors: Köse, Melis, Canda, Ebru, Kagnici, Mehtap, Uçar, Sema Kalkan, Çoker, Mahmut
Formato: Artigo
Idioma:Inglês
Publicado em: Hindawi 2017
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5447276/
https://ncbi.nlm.nih.gov/pubmed/28589054
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2017/1045031
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