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A Patient with MSUD: Acute Management with Sodium Phenylacetate/Sodium Benzoate and Sodium Phenylbutyrate

In treatment of metabolic imbalances caused by maple syrup urine disease (MSUD), peritoneal dialysis, and hemofiltration, pharmacological treatments for elimination of toxic metabolites can be used in addition to basic dietary modifications. Therapy with sodium phenylacetate/benzoate or sodium pheny...

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Dettagli Bibliografici
Pubblicato in:Case Rep Pediatr
Autori principali: Köse, Melis, Canda, Ebru, Kagnici, Mehtap, Uçar, Sema Kalkan, Çoker, Mahmut
Natura: Artigo
Lingua:Inglês
Pubblicazione: Hindawi 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5447276/
https://ncbi.nlm.nih.gov/pubmed/28589054
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2017/1045031
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