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Pancreatic Kaposiform Hemangioendothelioma Not Responding to Sirolimus

Background  Kaposiform hemangioendothelioma (KHE) is a vascular tumor frequently associated with Kasabach–Merritt phenomenon (KMP), characterized by severe thrombocytopenia and consumptive coagulopathy. Visceral involvement in KHE is rare. In our recent experience, sirolimus has shown to be an effec...

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Bibliografske podrobnosti
izdano v:European J Pediatr Surg Rep
Main Authors: Triana, Paloma Junco, Dore, Mariela, Nuñez, Vanesa Cerezo, Jimenez, Javier Gomez, Miguel, Miriam Ferrero, Díaz, Mercedes González, Ricardo, Joan Novo, Andres, Ane, Lopez Santamaria, Manuel, Lopez-Gutierrez, Juan Carlos
Format: Artigo
Jezik:Inglês
Izdano: Georg Thieme Verlag KG 2017
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC5533608/
https://ncbi.nlm.nih.gov/pubmed/28761800
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1055/s-0037-1604358
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