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Pancreatic Kaposiform Hemangioendothelioma Not Responding to Sirolimus

Background  Kaposiform hemangioendothelioma (KHE) is a vascular tumor frequently associated with Kasabach–Merritt phenomenon (KMP), characterized by severe thrombocytopenia and consumptive coagulopathy. Visceral involvement in KHE is rare. In our recent experience, sirolimus has shown to be an effec...

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Detalhes bibliográficos
Publicado no:European J Pediatr Surg Rep
Main Authors: Triana, Paloma Junco, Dore, Mariela, Nuñez, Vanesa Cerezo, Jimenez, Javier Gomez, Miguel, Miriam Ferrero, Díaz, Mercedes González, Ricardo, Joan Novo, Andres, Ane, Lopez Santamaria, Manuel, Lopez-Gutierrez, Juan Carlos
Formato: Artigo
Idioma:Inglês
Publicado em: Georg Thieme Verlag KG 2017
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5533608/
https://ncbi.nlm.nih.gov/pubmed/28761800
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1055/s-0037-1604358
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