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Febuxostat for the Prevention of Recurrent 2,8-dihydroxyadenine Nephropathy due to Adenine Phosphoribosyltransferase Deficiency Following Kidney Transplantation

Adenine phosphoribosyltransferase (APRT) deficiency is a rare autosomal recessive disorder that results in irreversible renal damage due to 2,8-dihydroxyadenine (DHA) nephropathy. A 28-year-old man underwent living-related kidney transplantation for chronic kidney disease of unknown etiology. Numero...

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Dettagli Bibliografici
Pubblicato in:Intern Med
Autori principali: Nanmoku, Koji, Kurosawa, Akira, Shinzato, Takahiro, Shimizu, Toshihiro, Kimura, Takaaki, Yagisawa, Takashi
Natura: Artigo
Lingua:Inglês
Pubblicazione: The Japanese Society of Internal Medicine 2017
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5498204/
https://ncbi.nlm.nih.gov/pubmed/28566603
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2169/internalmedicine.56.8142
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