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Do Some Patients With Seckel Syndrome Have Hematological Problems and/or Chromosome Breakage?

We report on a 12-yr-old female and a 14-yr-old male with Seckel syndrome. The 12-yr-old female had pancytopenia, which is seen occasionally in patients with Seckel syndrome and is also a feature of Fanconi anemia, a well-recognized autosomal recessive dwarfism syndrome with chromosome instability....

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Библиографические подробности
Опубликовано в: :Am J Med Genet
Главные авторы: Butler, Merlin G., Hall, Bryan D., Maclean, Ronald N., Lozzio, Carmen B.
Формат: Artigo
Язык:Inglês
Опубликовано: 1987
Предметы:
Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC5494982/
https://ncbi.nlm.nih.gov/pubmed/3115102
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/ajmg.1320270318
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