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The clinical spectrum of Erdheim-Chester disease: an observational cohort study

Erdheim-Chester disease (ECD) is a rare, potentially fatal multiorgan myeloid neoplasm occurring mainly in adults. The diagnosis is established by clinical, radiologic, and histologic findings; ECD tumors contain foamy macrophages that are CD68(+), CD163(+), CD1a(−), and frequently S100(−). The purp...

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Detalles Bibliográficos
Publicado en:Blood Adv
Main Authors: Estrada-Veras, Juvianee I., O’Brien, Kevin J., Boyd, Louisa C., Dave, Rahul H., Durham, Benjamin H., Xi, Liqiang, Malayeri, Ashkan A., Chen, Marcus Y., Gardner, Pamela J., Alvarado Enriquez, Jhonell R., Shah, Nikeith, Abdel-Wahab, Omar, Gochuico, Bernadette R., Raffeld, Mark, Jaffe, Elaine S., Gahl, William A.
Formato: Artigo
Idioma:Inglês
Publicado: American Society of Hematology 2017
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC5446206/
https://ncbi.nlm.nih.gov/pubmed/28553668
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1182/bloodadvances.2016001784
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