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The clinical spectrum of Erdheim-Chester disease: an observational cohort study

Erdheim-Chester disease (ECD) is a rare, potentially fatal multiorgan myeloid neoplasm occurring mainly in adults. The diagnosis is established by clinical, radiologic, and histologic findings; ECD tumors contain foamy macrophages that are CD68(+), CD163(+), CD1a(−), and frequently S100(−). The purp...

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Dettagli Bibliografici
Pubblicato in:Blood Adv
Autori principali: Estrada-Veras, Juvianee I., O’Brien, Kevin J., Boyd, Louisa C., Dave, Rahul H., Durham, Benjamin H., Xi, Liqiang, Malayeri, Ashkan A., Chen, Marcus Y., Gardner, Pamela J., Alvarado Enriquez, Jhonell R., Shah, Nikeith, Abdel-Wahab, Omar, Gochuico, Bernadette R., Raffeld, Mark, Jaffe, Elaine S., Gahl, William A.
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Society of Hematology 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5446206/
https://ncbi.nlm.nih.gov/pubmed/28553668
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1182/bloodadvances.2016001784
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