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Motor neuron vulnerability and resistance in amyotrophic lateral sclerosis
In the fatal disease—amyotrophic lateral sclerosis (ALS)—upper (corticospinal) motor neurons (MNs) and lower somatic MNs, which innervate voluntary muscles, degenerate. Importantly, certain lower MN subgroups are relatively resistant to degeneration, even though pathogenic proteins are typically ubi...
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| Publicado en: | Acta Neuropathol |
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| Autores principales: | , , |
| Formato: | Artigo |
| Lenguaje: | Inglês |
| Publicado: |
Springer Berlin Heidelberg
2017
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| Materias: | |
| Acceso en línea: | https://ncbi.nlm.nih.gov/pmc/articles/PMC5427160/ https://ncbi.nlm.nih.gov/pubmed/28409282 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s00401-017-1708-8 |
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