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Cardiopulmonary dysfunction in patients with limb‐girdle muscular dystrophy 2A

Introduction: Little is known about the frequency of cardiopulmonary failure in limb‐girdle muscular dystrophy type 2A (calpainopathy) patients, although some studies have reported severe cardiomyopathy or respiratory failure. Methods: To clarify the frequency of cardiopulmonary dysfunction in this...

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Publicado en:Muscle Nerve
Autores principales: Mori‐Yoshimura, Madoka, Segawa, Kazuhiko, Minami, Narihiro, Oya, Yasushi, Komaki, Hirohumi, Nonaka, Ikuya, Nishino, Ichizo, Murata, Miho
Formato: Artigo
Lenguaje:Inglês
Publicado: John Wiley and Sons Inc. 2016
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC5396288/
https://ncbi.nlm.nih.gov/pubmed/27500519
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/mus.25369
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