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Rimmed Vacuoles in Becker Muscular Dystrophy Have Similar Features with Inclusion Myopathies

Rimmed vacuoles in myofibers are thought to be due to the accumulation of autophagic vacuoles, and can be characteristic in certain myopathies with protein inclusions in myofibers. In this study, we performed a detailed clinical, molecular, and pathological characterization of Becker muscular dystro...

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Dades bibliogràfiques
Autors principals: Momma, Kazunari, Noguchi, Satoru, Malicdan, May Christine V., Hayashi, Yukiko K., Minami, Narihiro, Kamakura, Keiko, Nonaka, Ikuya, Nishino, Ichizo
Format: Artigo
Idioma:Inglês
Publicat: Public Library of Science 2012
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3522649/
https://ncbi.nlm.nih.gov/pubmed/23251671
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0052002
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