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Lung structure and function similarities between primary ciliary dyskinesia and mild cystic fibrosis: a pilot study

BACKGROUND: Primary ciliary dyskinesia (PCD) and cystic fibrosis (CF) are increasingly compared. There are no chest magnetic resonance imaging (MRI) comparative studies of PCD and CF. We assessed clinical, functional, microbiological and MRI findings in PCD and mild CF patients in order to evaluate...

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Dades bibliogràfiques
Publicat a:Ital J Pediatr
Autors principals: Maglione, Marco, Montella, Silvia, Mollica, Carmine, Carnovale, Vincenzo, Iacotucci, Paola, De Gregorio, Fabiola, Tosco, Antonella, Cervasio, Mariarosaria, Raia, Valeria, Santamaria, Francesca
Format: Artigo
Idioma:Inglês
Publicat: BioMed Central 2017
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5389053/
https://ncbi.nlm.nih.gov/pubmed/28403885
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13052-017-0351-2
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