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Lung structure and function similarities between primary ciliary dyskinesia and mild cystic fibrosis: a pilot study

BACKGROUND: Primary ciliary dyskinesia (PCD) and cystic fibrosis (CF) are increasingly compared. There are no chest magnetic resonance imaging (MRI) comparative studies of PCD and CF. We assessed clinical, functional, microbiological and MRI findings in PCD and mild CF patients in order to evaluate...

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Publicado en:Ital J Pediatr
Main Authors: Maglione, Marco, Montella, Silvia, Mollica, Carmine, Carnovale, Vincenzo, Iacotucci, Paola, De Gregorio, Fabiola, Tosco, Antonella, Cervasio, Mariarosaria, Raia, Valeria, Santamaria, Francesca
Formato: Artigo
Idioma:Inglês
Publicado: BioMed Central 2017
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC5389053/
https://ncbi.nlm.nih.gov/pubmed/28403885
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13052-017-0351-2
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