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CFTR structure and function: is there a role in the kidney?

Cystic fibrosis (CF) is a lethal autosomal recessive genetic disease caused by mutations in the CF transmembrane conductance regulator (CFTR). Mutations in the CFTR gene may result in a defective protein processing that leads to changes in function and regulation of this chloride channel. Despite of...

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Dettagli Bibliografici
Pubblicato in:Biophys Rev
Autori principali: Souza-Menezes, J., Morales, M. M.
Natura: Artigo
Lingua:Inglês
Pubblicazione: Springer-Verlag 2009
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5387792/
https://ncbi.nlm.nih.gov/pubmed/28510151
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s12551-008-0002-3
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