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From Lysosomal Storage Diseases to NKT Cell Activation and Back

Lysosomal storage diseases (LSDs) are inherited metabolic disorders characterized by the accumulation of different types of substrates in the lysosome. With a multisystemic involvement, LSDs often present a very broad clinical spectrum. In many LSDs, alterations of the immune system were described....

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Dades bibliogràfiques
Publicat a:Int J Mol Sci
Autors principals: Pereira, Cátia S., Ribeiro, Helena, Macedo, M. Fatima
Format: Artigo
Idioma:Inglês
Publicat: MDPI 2017
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5372518/
https://ncbi.nlm.nih.gov/pubmed/28245613
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms18030502
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