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International, evidence-based consensus diagnostic criteria for HHV-8–negative/idiopathic multicentric Castleman disease

Human herpesvirus-8 (HHV-8)–negative, idiopathic multicentric Castleman disease (iMCD) is a rare and life-threatening disorder involving systemic inflammatory symptoms, polyclonal lymphoproliferation, cytopenias, and multiple organ system dysfunction caused by a cytokine storm often including interl...

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Pubblicato in:Blood
Autori principali: Fajgenbaum, David C., Uldrick, Thomas S., Bagg, Adam, Frank, Dale, Wu, David, Srkalovic, Gordan, Simpson, David, Liu, Amy Y., Menke, David, Chandrakasan, Shanmuganathan, Lechowicz, Mary Jo, Wong, Raymond S. M., Pierson, Sheila, Paessler, Michele, Rossi, Jean-François, Ide, Makoto, Ruth, Jason, Croglio, Michael, Suarez, Alexander, Krymskaya, Vera, Chadburn, Amy, Colleoni, Gisele, Nasta, Sunita, Jayanthan, Raj, Nabel, Christopher S., Casper, Corey, Dispenzieri, Angela, Fosså, Alexander, Kelleher, Dermot, Kurzrock, Razelle, Voorhees, Peter, Dogan, Ahmet, Yoshizaki, Kazuyuki, van Rhee, Frits, Oksenhendler, Eric, Jaffe, Elaine S., Elenitoba-Johnson, Kojo S. J., Lim, Megan S.
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Society of Hematology 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5364342/
https://ncbi.nlm.nih.gov/pubmed/28087540
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1182/blood-2016-10-746933
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