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International, evidence-based consensus diagnostic criteria for HHV-8–negative/idiopathic multicentric Castleman disease

Human herpesvirus-8 (HHV-8)–negative, idiopathic multicentric Castleman disease (iMCD) is a rare and life-threatening disorder involving systemic inflammatory symptoms, polyclonal lymphoproliferation, cytopenias, and multiple organ system dysfunction caused by a cytokine storm often including interl...

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Publicat a:Blood
Autors principals: Fajgenbaum, David C., Uldrick, Thomas S., Bagg, Adam, Frank, Dale, Wu, David, Srkalovic, Gordan, Simpson, David, Liu, Amy Y., Menke, David, Chandrakasan, Shanmuganathan, Lechowicz, Mary Jo, Wong, Raymond S. M., Pierson, Sheila, Paessler, Michele, Rossi, Jean-François, Ide, Makoto, Ruth, Jason, Croglio, Michael, Suarez, Alexander, Krymskaya, Vera, Chadburn, Amy, Colleoni, Gisele, Nasta, Sunita, Jayanthan, Raj, Nabel, Christopher S., Casper, Corey, Dispenzieri, Angela, Fosså, Alexander, Kelleher, Dermot, Kurzrock, Razelle, Voorhees, Peter, Dogan, Ahmet, Yoshizaki, Kazuyuki, van Rhee, Frits, Oksenhendler, Eric, Jaffe, Elaine S., Elenitoba-Johnson, Kojo S. J., Lim, Megan S.
Format: Artigo
Idioma:Inglês
Publicat: American Society of Hematology 2017
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5364342/
https://ncbi.nlm.nih.gov/pubmed/28087540
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1182/blood-2016-10-746933
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