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Juvenile and adult metachromatic leukodystrophy: partial restoration of arylsulfatase A (cerebroside sulfatase) activity by inhibitors of thiol proteinases.

Arylsulfatase A polypeptides were examined in cultured fibroblasts from a patient with juvenile metachromatic leukodystrophy and three patients with the adult form of the disease, with the aid of metabolic labeling and immunoprecipitation. The mutant cells were severely deficient in the arylsulfatas...

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Detalles Bibliográficos
Publicado en:Proc Natl Acad Sci U S A
Main Authors: von Figura, K, Steckel, F, Hasilik, A
Formato: Artigo
Idioma:Inglês
Publicado: National Academy of Sciences 1983
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Acceso en liña:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC534361/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/6136972/
https://ncbi.nlm.nih.govhttps://doi.org/10.1073/pnas.80.19.6066
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