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Disease manifestations and burden of illness in patients with acid sphingomyelinase deficiency (ASMD)

Acid sphingomyelinase deficiency (ASMD), a rare lysosomal storage disease, is an autosomal recessive genetic disorder caused by different SMPD1 mutations. Historically, ASMD has been classified as Niemann-Pick disease (NPD) types A (NPD A) and B (NPD B). NPD A is associated with a uniformly devastat...

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Detalhes bibliográficos
Publicado no:Orphanet J Rare Dis
Main Authors: McGovern, Margaret M., Avetisyan, Ruzan, Sanson, Bernd-Jan, Lidove, Olivier
Formato: Artigo
Idioma:Inglês
Publicado em: BioMed Central 2017
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5322625/
https://ncbi.nlm.nih.gov/pubmed/28228103
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-017-0572-x
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