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A saposin deficiency model in Drosophila: Lysosomal storage, progressive neurodegeneration and sensory physiological decline

Saposin deficiency is a childhood neurodegenerative lysosomal storage disorder (LSD) that can cause premature death within three months of life. Saposins are activator proteins that promote the function of lysosomal hydrolases that mediate the degradation of sphingolipids. There are four saposin pro...

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Dettagli Bibliografici
Pubblicato in:Neurobiol Dis
Autori principali: Hindle, Samantha J., Hebbar, Sarita, Schwudke, Dominik, Elliott, Christopher J.H., Sweeney, Sean T.
Natura: Artigo
Lingua:Inglês
Pubblicazione: Academic Press 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5319729/
https://ncbi.nlm.nih.gov/pubmed/27913291
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.nbd.2016.11.012
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