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Mitochondrial Dysregulation Secondary to Endoplasmic Reticulum Stress in Autosomal Dominant Tubulointerstitial Kidney Disease – UMOD (ADTKD-UMOD)

‘Autosomal dominant tubulointerstitial kidney disease – UMOD’ (ADTKD-UMOD) is caused by impaired maturation and secretion of mutant uromodulin (UMOD) in thick ascending limb of Henle loop (TAL) cells, resulting in endoplasmic reticulum (ER) stress and unfolded protein response (UPR). To gain insight...

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Dettagli Bibliografici
Pubblicato in:Sci Rep
Autori principali: Kemter, Elisabeth, Fröhlich, Thomas, Arnold, Georg J., Wolf , Eckhard, Wanke, Rüdiger
Natura: Artigo
Lingua:Inglês
Pubblicazione: Nature Publishing Group 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5318959/
https://ncbi.nlm.nih.gov/pubmed/28220896
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/srep42970
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