Cargando...

Prevalence, birth incidence, and penetrance of von Hippel–Lindau disease (vHL) in Denmark

Von Hippel–Lindau disease (vHL) is a rare hereditary tumour predisposition with multiorgan involvement that is not always easily recognized. The disease is reported to be almost fully penetrant at age 60 years. Previous estimates of vHL prevalence and incidence are all regional and vary widely. Most...

Descrición completa

Gardado en:
Detalles Bibliográficos
Publicado en:Eur J Hum Genet
Main Authors: Binderup, Marie Louise Mølgaard, Galanakis, Michael, Budtz-Jørgensen, Esben, Kosteljanetz, Michael, Luise Bisgaard, Marie
Formato: Artigo
Idioma:Inglês
Publicado: Nature Publishing Group 2017
Assuntos:
Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC5315510/
https://ncbi.nlm.nih.gov/pubmed/27966541
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/ejhg.2016.173
Tags: Engadir etiqueta
Sen Etiquetas, Sexa o primeiro en etiquetar este rexistro!