Caricamento...

Spectrum of mutations in aspartylglucosaminuria.

Aspartylglucosaminuria (AGU) is an inherited lysosomal storage disorder caused by the deficiency of aspartylglucosaminidase. We have earlier reported a single missense mutation (Cys163----Ser) to be responsible for 98% of the AGU alleles in the isolated Finnish population, which contains about 90% o...

Descrizione completa

Salvato in:
Dettagli Bibliografici
Autori principali: Ikonen, E, Aula, P, Grön, K, Tollersrud, O, Halila, R, Manninen, T, Syvänen, A C, Peltonen, L
Natura: Artigo
Lingua:Inglês
Pubblicazione: 1991
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC53106/
https://ncbi.nlm.nih.gov/pubmed/1722323
Tags: Aggiungi Tag
Nessun Tag, puoi essere il primo ad aggiungerne! !