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Flunarizine Rescues Reduced Lifespan in CLN3 Triple Knock-Out Caenorhabditis elegans Model of Batten Disease
CLN3 disease (Spielmeyer-Vogt-Sjogren-Batten disease, previously known as classic juvenile neuronal ceroid lipofuscinosis, NCL) is a pediatric-onset progressive neurodegenerative disease characterized by progressive vision loss, seizures, loss of cognitive and motor function, and early death. While...
Guardado en:
| Publicado en: | J Inherit Metab Dis |
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| Autores principales: | , , |
| Formato: | Artigo |
| Lenguaje: | Inglês |
| Publicado: |
2016
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| Materias: | |
| Acceso en línea: | https://ncbi.nlm.nih.gov/pmc/articles/PMC5309197/ https://ncbi.nlm.nih.gov/pubmed/27766444 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s10545-016-9986-1 |
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