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Syndrome de Meckel Gruber: à propos d’un cas rare

Meckel Gruber syndrome is a rare autosomal recessive polymalformation syndrome characterized by occipital encephalocele, polydactyly and cystic renal dysplasia. Ultrasound is, at present, the best tool for prenatal screening of this lethal polymalformation and diagnosys is confirmed by karyotyping....

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Pubblicato in:Pan Afr Med J
Autori principali: Itchimouh, Sanaa, Khabtou, Karima, Mahdaoui, Sakher, Boufettal, Houssine, Samouh, Naima
Natura: Artigo
Lingua:Inglês
Pubblicazione: The African Field Epidemiology Network 2016
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5268799/
https://ncbi.nlm.nih.gov/pubmed/28154732
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.11604/pamj.2016.25.43.9696
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